GKD Anest Yoð Bak Dern Derg. 2013; 19(4): 214-217 | DOI: 10.5222/GKDAD.2013.214

Pulmonary Hypertension Crisis in Pediatric Patient Undergoing Congenital Heart Surgery: Case Report

Dilek Altun¹, Þule Turgut Balcý¹, Emre Özker², Bülent Sarýtaþ², Canan Ayabakan³, Rýza Türköz², Ayda Türköz^1
1Baskent University, Departmant Of Anesthesiology And Reanimation, Istanbul, Turkey
²Baskent University, Departmant Of Cardiovascular Surgery, Istanbul, Turkey
³Baskent University, Departmant Of Pediatric Cardiology, Istanbul, Turkey

Pulmonary arterial hypertension (PAH) with increased pulmonary vascular resistance (PVR), is a frequent complication of congenital heart diseases (CHD). PH, is characterised by the chronic elevation of pulmonary artery pressure and pulmonary vascular resistance leading to right ventricular enlargement and hypertrophy 1-2. Vasoconstriction of pulmonary vessels plays an important role in the early prognosis in children with congenital heart disease who has pulmonary hypertension.
In this case report, we have reported a case who has undergone aortic interruption operation and successfully treated for the hypertensive crisis developing in the postoperative period.

Keywords: Pulmonary hypertension, pulmonary hypertensive crisis, congenital heart diseases, sildenafil

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Konjenital Kalp Cerrahisi Geçiren Pediyatrik Olguda Geliþen Pulmoner Hipertansif Kriz: Olgu Sunumu

Dilek Altun¹, Þule Turgut Balcý¹, Emre Özker², Bülent Sarýtaþ², Canan Ayabakan³, Rýza Türköz², Ayda Türköz^1
1Baþkent Üniversitesi, Anesteziyoloji Ve Reanimasyon Anabilim Dalý, Ýstanbul
²Baþkent Üniversitesi, Kalp Damar Cerrahisi Ana Bilim Dalý, Ýstanbul
³Baþkent Üniversitesi, Pediyatrik Kardiyoloji Ana Bilim Dalý, Ýstanbul

Pulmoner vasküler rezistansýn (PVR) artmasýyla beraber olan pulmoner hipertansiyon (PH) konjenital kalp hastalýklarýnýn (KKH) sýk görülen bir kompilkasyonudur. PH, pulmoner arter basýncý ve pulmoner vasküler rezistansta artýþ ile karakterize olup, sað ventriküler geniþleme ve hipertrofiye yol açar (1-2). PH’sý olan doðuþtan kalp hastalýklý çocuklarda ameliyat sonrasý pulmoner damarlarda oluþan vazokonstriksiyon hastanýn erken dönem prognozunda önemli rol oynamaktadýr3. Bu vaka sunumumuzda, aortik interuption nedeniyle ameliyat edilen, postoperatif dönemde hipertansif kriz geliþen ve baþarýlý bir þekilde tedavi edilen olgu sunulmuþtur.

Anahtar Kelimeler: Pulmoner hipertansiyon, pulmoner hipertansif kriz, konjenital kalp hastalýðý, sildenafil

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